DOI: https://doi.org/10.36347/sjmcr.2025.v13i06.032

Pages: 1431-1436

Moyamoya Disease (MMD) is a rare and extremely severe chronic cerebrovascular disorder characterized by progressive stenosis of the internal carotid artery and the development of an abnormal vascular network at the base of the brain. It presents clinically with ischemic strokes or hemorrhages. The case reported is that of a 47-year-old woman admitted for a subarachnoid hemorrhage. Imaging revealed a bilateral form of MMD. The patient received supportive medical treatment (mechanical ventilation, nimodipine) and an external ventricular drainage procedure, but the outcome was unfavorable due to the occurrence of cerebral ischemia, ultimately resulting in death. This case illustrates a rare presentation of MMD and highlights the severity of the disease progression in the absence of early revascularization, as well as the importance of prompt diagnosis and specialized intervention.