DOI: https://doi.org/10.36347/sasjs.2025.v11i07.012

Pages: 833-838

Caroli’s disease is a rare condition. It is characterized by multifocal dilatations of intrahepatic segmental bile ducts. This pathology can be complicated by lithiasis and hepatic abscesses. It is most often diffused, but can be localized mainly in the left lobe. We report a case of left monolobar Caroli’s disease revealed by a febrile mild jaundice in a patient in his sixties, with an interval of 2 months between the first symptom and the diagnosis, which was suggested by compelling MRI findings and confirmed by the anatomopathological study. The patient underwent a left hepatic lobectomy without apparent complications the following 6 months. Despite the rarity of Caroli's disease, this case illustrates its typical form in the literature.