DOI: https://doi.org/10.36347/sjmcr.2025.v13i11.046

Pages: 2854-2857

Background: Unilateral pulmonary artery agenesis (UPAA) is a rare congenital vascular anomaly resulting from an embryologic failure of the sixth aortic arch to connect with the pulmonary trunk. Its clinical presentation is variable, ranging from severe respiratory symptoms in childhood to incidental discovery in asymptomatic adults. We report the fortuitous detection of this condition in an adult male who presented with grade II dyspnea and chest pain lasting for one week. Contrast-enhanced chest CT revealed absence of the right pulmonary artery with ipsilateral pulmonary hypoplasia. This case underscores the key role of CT scan in identifying rare vascular anomalies, even in mildly symptomatic patients.